BCKDHA

gene product
MSU, OVD1A
The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Sep 2009]
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33 antibodies from 12 providers.

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AntibodyRefsTypeWBELIFIPIHFC
GeneTex
3 antibodies
GTX111382Polyclonal
GTX45109Polyclonal
Thermo Fisher Scientific Pierce
1 antibody
PA5-29300Polyclonal
Aviva Systems Biology
2 antibodies
OAAB03929Polyclonal
ARP56119_P050Polyclonal
Novus Biologicals
5 antibodies
NBP1-81022Polyclonal
H00000593-A01Polyclonal
Atlas Antibodies
1 antibody
HPA036640Polyclonal
Bethyl Laboratories, Inc.
3 antibodies
A303-789APolyclonal
A303-790APolyclonal
antibodies-online
7 antibodies
ABIN390811Polyclonal
ABIN787301Polyclonal
Abnova Corporation
3 antibodies
H00000593-A01Polyclonal
H00000593-B01Polyclonal
Acris Antibodies GmbH
4 antibodies
AP17149PU-NPolyclonal
AP17149CP-NPolyclonal
Epitomics
1 antibody
T1759Polyclonal
Creative Biomart
2 antibodies
CPBT-27177MHPolyclonal
CPBT-51745RHPolyclonal
LifeSpan BioSciences, Inc.
1 antibody
LS-C111808Polyclonal (Antigen purified)