Tissue expression
Cell line expression
Protein structure
LRPPRC
Leucine rich pentatricopeptide repeat containingGP130, LRP130, LSFC
This gene encodes a leucine-rich protein that has multiple pentatricopeptide repeats (PPR). The precise role of this protein is unknown but studies suggest it may play a role in cytoskeletal organization, vesicular transport, or in transcriptional regulation of both nuclear and mitochondrial genes. The protein localizes primarily to mitochondria and is predicted to have an N-terminal mitochondrial targeting sequence. Mutations in this gene are associated with the French-Canadian type of Leigh syndrome. [provided by RefSeq, Mar 2012]
Top validated antibodies |
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Proteintech Group | ![]() |
32 references | Polyclonal |
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Boster Biological Technology | ![]() |
1 references | Polyclonal |
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Invitrogen Antibodies | ![]() |
Polyclonal |
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Atlas Antibodies | ![]() |
Polyclonal |
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LSBio | ![]() |
Polyclonal |
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