Tissue expression
Cell line expression
Protein structure
FXN
FrataxinCyaY, FA, FARR, FRDA, X25
This nuclear gene encodes a mitochondrial protein which belongs to the FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA from 8-33 repeats to >90 repeats results in Friedreich ataxia. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Jul 2016]
Top validated antibodies |
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Invitrogen Antibodies | 45-6300 | 1 references | Monoclonal |
WB
ICC
IHC
FC
OA
|
|
OriGene | TA504254 | Monoclonal |
WB
ICC
IHC
FC |
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antibodies-online | ABIN4312566 | Monoclonal |
WB
ICC
IHC
FC |
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LSBio | LS-C331670 | Polyclonal |
WB
ICC
IHC
|
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Novus Biologicals | NBP2-01743 | Monoclonal |
WB
ICC
IHC
FC |
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Supportive data in Antibodypedia
Data presented on provider website
Data in Antibodypedia (inconclusive)
Recommended by provider