Tissue expression
Cell line expression
Protein structure
TMEM126B
Transmembrane protein 126BHT007
This gene encodes a mitochondrial transmembrane protein which is a component of the mitochondrial complex I assembly complex. The encoded protein serves as an assembly factor that is required for formation of the membrane arm of the complex. It interacts with NADH dehydrogenase [ubiquinone] 1 alpha subcomplex assembly factor 13. Naturally occurring mutations in this gene are associated with isolated complex I deficiency. A pseudogene of this gene has been defined on chromosome 9. [provided by RefSeq, Apr 2017]
Top validated antibodies |
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Atlas Antibodies | HPA014480 | Polyclonal |
WB
ICC
IHC
|
||
Invitrogen Antibodies | PA5-53178 | Polyclonal |
WB
ICC
IHC
|
||
Novus Biologicals | NBP1-83158 | Polyclonal |
WB
ICC
IHC
|
||
antibodies-online | ABIN4360576 | Polyclonal |
WB
ICC
IHC
|
||
Abnova Corporation | H00055863-D01 | Polyclonal |
WB
IP |
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Supportive data in Antibodypedia
Data presented on provider website
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Recommended by provider