Tissue expression
Cell line expression
Protein structure
AASS
Aminoadipate-semialdehyde synthaseLKRSDH, LORSDH
This gene encodes a bifunctional enzyme that catalyzes the first two steps in the mammalian lysine degradation pathway. The N-terminal and the C-terminal portions of this enzyme contain lysine-ketoglutarate reductase and saccharopine dehydrogenase activity, respectively, resulting in the conversion of lysine to alpha-aminoadipic semialdehyde. Mutations in this gene are associated with familial hyperlysinemia. [provided by RefSeq, Jul 2008]
Top validated antibodies |
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Atlas Antibodies | HPA020728 | 1 references | Polyclonal |
WB
ICC
IHC
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NSJ Bioreagents | RQ6595 | Polyclonal |
WB
EL
ICC
IHC
FC
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Novus Biologicals | NBP1-82832 | 1 references | Polyclonal |
WB
ICC
IHC
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Biorbyt | orb865481 | Polyclonal |
WB
EL
ICC
IHC
FC
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antibodies-online | ABIN950197 | 2 references | Polyclonal |
WB
FC |
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