BS3518

antibody from Bioworld Technology, Inc

Targeting: SGCB A3b, LGMD2E, SGC

Immunohistochemistry

Antibody data

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Validation data

Product number: BS3518 - Provider product page
Provider: Bioworld Technology, Inc
Proper citation: Bioworld Technology Cat#BS3518, RRID:AB_1663035
Product name: Sarcoglycan ÉÇ (V136) polyclonal antibody
Antibody type: Polyclonal
Antigen: Synthetic peptide, corresponding to amino acids 102-158 of Human Sarcoglycan-ÉÇ.
Description: Four sarcoglycan subunit proteins, designated Ï«-, ÉÇ-, ÎÛ- and Ñ´-sarcoglycan, form a complex on the skeletal muscle cell surface membrane. A genetic defect in any one of these proteins causes the loss or marked decrease of the whole sarcoglycan complex, which is observed in the autosomal recessive muscular dystrophy, sarcoglycanopathy. In smooth muscle, ÉÇ- and Ñ´-sarcoglycans are associated with ÷-sarcoglycan, a glycoprotein homologous to Ï«-sarcoglycan. Additionally, a complete deficiency in Ñ´-sarcoglycan is the cause of the Syrian hamster BIO.14 cardiomyopathy.
Reactivity: Human, Mouse, Rat
Host: Rabbit
Isotype: IgG
Vial size: 100ul
Concentration: 1 mg/ml
Storage: Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.

SGCB protein structure - BS3518 shown in red.