Tissue expression
Cell line expression
Protein structure
BBOX1
Gamma-butyrobetaine hydroxylase 1BBH, BBOX, G-BBH, gamma-BBH
This gene encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation. [provided by RefSeq, Jul 2008]
Top validated antibodies |
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LSBio | ![]() |
Monoclonal |
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Invitrogen Antibodies | ![]() |
1 references | Polyclonal |
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antibodies-online | ![]() |
Monoclonal |
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OriGene | ![]() |
Monoclonal |
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Proteintech Group | ![]() |
1 references | Polyclonal |
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