Tissue expression
Cell line expression
Protein structure
BBOX1
Gamma-butyrobetaine hydroxylase 1BBH, BBOX, G-BBH, gamma-BBH
This gene encodes gamma butyrobetaine hydroxylase which catalyzes the formation of L-carnitine from gamma-butyrobetaine, the last step in the L-carnitine biosynthetic pathway. Carnitine is essential for the transport of activated fatty acids across the mitochondrial membrane during mitochondrial beta-oxidation. [provided by RefSeq, Jul 2008]
Top validated antibodies |
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Invitrogen Antibodies | PA5-21477 | 1 references | Polyclonal |
WB
ICC
IHC
OA |
|
antibodies-online | ABIN2670949 | Monoclonal |
WB
ICC
IHC
FC |
||
OriGene | UM500084 | Monoclonal |
WB
ICC
IHC
OA |
||
LSBio | LS-C174488 | Monoclonal |
WB
ICC
IHC
|
||
Novus Biologicals | NBP1-32327 | 1 references | Polyclonal |
WB
ICC
IHC
|
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Supportive data in Antibodypedia
Data presented on provider website
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Recommended by provider