ABIN954086
antibody from antibodies-online
Targeting: TWNK
C10orf2, FLJ21832, IOSCA, PEO, PEO1, TWINKLE, TWINL
Antibody data
- Antibody Data
- Antigen structure
- References [2]
- Comments [0]
- Validations
- Western blot [1]
- Immunohistochemistry [1]
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Validation data
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- Product number
- ABIN954086 - Provider product page
- Provider
- antibodies-online
- Product name
- anti-Chromosome 10 Open Reading Frame 2 (C10ORF2) (AA 663-684), (C-Term) antibody
- Antibody type
- Polyclonal
- Description
- Affinity chromatography on Protein A
- Reactivity
- Human
- Host
- Rabbit
- Epitope
- AA 663-684, C-Term
- Vial size
- 0.4 mL
- Storage
- Store the antibody undiluted at 2-8°C for one month or (in aliquots) at -20°C for longer.
- Handling
- Avoid repeated freezing and thawing.
Submitted references Disease variants of the human mitochondrial DNA helicase encoded by C10orf2 differentially alter protein stability, nucleotide hydrolysis, and helicase activity.
The clinical, histochemical, and molecular spectrum of PEO1 (Twinkle)-linked adPEO.
Longley MJ, Humble MM, Sharief FS, Copeland WC
The Journal of biological chemistry 2010 Sep 24;285(39):29690-702
The Journal of biological chemistry 2010 Sep 24;285(39):29690-702
The clinical, histochemical, and molecular spectrum of PEO1 (Twinkle)-linked adPEO.
Fratter C, Gorman GS, Stewart JD, Buddles M, Smith C, Evans J, Seller A, Poulton J, Roberts M, Hanna MG, Rahman S, Omer SE, Klopstock T, Schoser B, Kornblum C, Czermin B, Lecky B, Blakely EL, Craig K, Chinnery PF, Turnbull DM, Horvath R, Taylor RW
Neurology 2010 May 18;74(20):1619-26
Neurology 2010 May 18;74(20):1619-26
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Supportive validation
- Submitted by
- antibodies-online (provider)
- Main image
- Experimental details
- WB
Supportive validation
- Submitted by
- antibodies-online (provider)
- Main image
- Experimental details
- IHC