Antibody data
- Antibody Data
- Antigen structure
- References [1]
- Comments [0]
- Validations [0]
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- Product number
- MA1-2004 - Provider product page
- Provider
- Invitrogen Antibodies
- Product name
- Anti-PKP1 Monoclonal Antibody (10B2)
- Antibody type
- Monoclonal
- Antigen
- Other
- Description
- MA1-20040 detects fibrinogen in human samples. MA1-20040 has been successfully used in ELISA and Western blot procedures. The MA1-20040 immunogen is fibrin degradation products.
- Reactivity
- Human
- Host
- Mouse
- Isotype
- IgG
- Antibody clone number
- 10B2
- Vial size
- 200 µg
- Concentration
- 1 mg/ml
- Storage
- -20° C, Avoid Freeze/Thaw Cycles
Submitted references Homozygous splice site mutations in PKP1 result in loss of epidermal plakophilin 1 expression and underlie ectodermal dysplasia/skin fragility syndrome in two consanguineous families.
Sprecher E, Molho-Pessach V, Ingber A, Sagi E, Indelman M, Bergman R
The Journal of investigative dermatology 2004 Mar;122(3):647-51
The Journal of investigative dermatology 2004 Mar;122(3):647-51
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