BS8978

antibody from Bioworld Technology, Inc
Targeting: COX10
Provider product page for BS8978
Western blot
Immunohistochemistry

Antibody data

Product number
BS8978 - Provider product page
Provider
Bioworld Technology, Inc
Product name
COX10 polyclonal antibody
Antibody type
Polyclonal
Antigen
Protoheme IX farnesyltransferase; mitochondrial; Heme O synthase; COX10
Description
Defects in COX10 are a cause of mitochondrial complex IV deficiency (MT-C4D) [MIM:220110]; also known as cytochrome c oxidase deficiency. A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, excercise intolerance, developmental delay, delayed motor development and mental retardation. A subset of patients manifest Leigh syndrome.
Reactivity
Human, Mouse, Rat
Host
Rabbit
Isotype
IgG
Vial size
100ul
Concentration
1 mg/ml
Storage
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
COX10 protein structure - BS8978 shown in red.