BS8101

antibody from Bioworld Technology, Inc
Targeting: BTD
Provider product page for BS8101
Western blot
Immunohistochemistry

Antibody data

Product number
BS8101 - Provider product page
Provider
Bioworld Technology, Inc
Product name
BTD polyclonal antibody
Antibody type
Polyclonal
Antigen
Recombinant full length Human BTD.
Description
Biotin, also known as vitamin B7, is an essential water-soluble vitamin that is a cofactor in glucogenesis and in the metabolism of fatty acids and leucine. Biotinidase is a 523 amino acid enzyme that catalyzes the hydrolysis of biocytin to biotin and lysine. Secreted into extracellular space, biotinidase is expressed in liver, heart, placenta, brain, skeletal muscle, pancreas and kidney. Biotinidase contains one carbon-nitrogen hydrolase domain, which is involved in the reduction of organic nitrogen compounds and ammonia production. Defects in the gene encoding biotinidase are the cause of biotinidase deficiency, which is characterized by skin rash, ataxia, seizures, hearing loss, hypotonia and optic atrophy. These symptoms are due to the individual£ªs inability to reutilize biotin and can, therefore, typically be treated with the addition of free biotin.
Reactivity
Human
Host
Rabbit
Isotype
IgG
Vial size
100ul
Concentration
1 mg/ml
Storage
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
BTD protein structure - BS8101 shown in red.