BS8104

antibody from Bioworld Technology, Inc
Targeting: FUCA1
Provider product page for BS8104
Western blot
Immunohistochemistry

Antibody data

Product number
BS8104 - Provider product page
Provider
Bioworld Technology, Inc
Product name
FUCA1 polyclonal antibody
Antibody type
Polyclonal
Antigen
Recombinant full length Human FUCA1.
Description
FUCA1 (fucosidase, Ï«-L-1, tissue) is a 466 amino acid membrane- and seminalassociated is ozyme that is a member of the glycosyl hydrolase 29 family. FUCA1 functions as a homotetramer and is responsible for hydrolyzing and reducing the carbohydrate moieties of glycoproteins in various tissues. Defects in the gene encoding FUCA1 result in fucosidosis, an autosomal recessive disorder caused by an accumulation of fucose-containing glycolipids and glycoproteins.Fucosidosis, a lysosomal storage disease, is characterized by neurologic deterioration, growth retardation, visceromegaly, and seizures. Early onset of fucosidosis causes coarse facial features, angiokeratoma corporis diffusum, spasticity, delayed psychomotor development and an unusual spondylometaphyseoepiphyseal dysplasia.
Reactivity
Human
Host
Rabbit
Isotype
IgG
Vial size
100ul
Concentration
1 mg/ml
Storage
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
FUCA1 protein structure - BS8104 shown in red.