HPA037701

antibody from Atlas Antibodies

Targeting: BCS1L BCS, BJS, h-BCS, Hs.6719

Western blot (Data presented on provider website)

Immunohistochemistry (Data presented on provider website)

Antibody Data

Product number

HPA037701

Provider

Atlas Antibodies

Proper citation

Atlas Antibodies Cat#HPA037701, RRID:AB_10805235

Product name

Anti-BCS1L

Antibody type

Polyclonal

Description

Polyclonal Antibody against Human BCS1L, Gene description: BC1 (ubiquinol-cytochrome c reductase) synthesis-like, Alternative Gene Names: BCS, BJS, h-BCS, Hs.6719, Validated applications: IHC, WB, Uniprot ID: Q9Y276, Storage: Store at +4°C for short term storage. Long time storage is recommended at -20°C.

Reactivity

Human

Host

Rabbit

Conjugate

Unconjugated

Isotype

IgG

Vial size

100 µl

Concentration

0.3 mg/ml

Storage

Store at +4°C for short term storage. Long time storage is recommended at -20°C.

Handling

The antibody solution should be gently mixed before use.

References

Submitted references

Respiratory chain complex III deficiency due to mutated BCS1L: a novel phenotype with encephalomyopathy, partially phenocopied in a Bcs1l mutant mouse model.

Tegelberg S, Tomašić N, Kallijärvi J, Purhonen J, Elmér E, Lindberg E, Nord DG, Soller M, Lesko N, Wedell A, Bruhn H, Freyer C, Stranneheim H, Wibom R, Nennesmo I, Wredenberg A, Eklund EA, Fellman V
Orphanet journal of rare diseases 2017 Apr 20;12(1):73