BS8302

antibody from Bioworld Technology, Inc
Targeting: HPS1 BLOC3S1, HPS
Provider product page for BS8302
Western blot
Immunocytochemistry
Immunohistochemistry

Antibody data

Product number
BS8302 - Provider product page
Provider
Bioworld Technology, Inc
Product name
HPS1 polyclonal antibody
Antibody type
Polyclonal
Antigen
Recombinant full length Human HPS1.
Description
Hermansky-Pudlak syndrome (HPS) is a rare, genetically heterogeneous, autosomal recessive disorder. It is characterized by oculocutaneous albinism, lysosomal storage defects and prolonged bleeding due to platelet storage pool deficiency. There are 10 HPS genes encoding HPS proteins that all interact within three distinct ubiquitously expressed protein complexes or biogenesis of lysosome-related organelle complexes. Defects in these genes cause HPS. HSP-1 is a component of multiple cytoplasmic organelles and is important for their normal development and function. It plays a role in intracellular protein sorting.
Reactivity
Human
Host
Rabbit
Isotype
IgG
Vial size
100ul
Concentration
1 mg/ml
Storage
Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze-thaw cycles.
HPS1 protein structure - BS8302 shown in red.