Tissue expression
Cell line expression
Protein structure
BFSP1
Beaded filament structural protein 1CP115, CP94, filensin, LIFL-H
This gene encodes a lens-specific intermediate filament-like protein named filensin. The encoded protein is expressed in lens fiber cells after differentiation has begun. This protein functions as a component of the beaded filament which is a cytoskeletal structure found in lens fiber cells. Mutations in this gene are the cause of autosomal recessive cortical juvenile-onset cataract. Alternate splicing results in multiple transcript variants. [provided by RefSeq, Jul 2013]
Top validated antibodies |
|||||
Atlas Antibodies | HPA040748 | Polyclonal |
WB
ICC
IHC
|
||
LSBio | LS-C155366 | Polyclonal |
WB
IHC |
||
Invitrogen Antibodies | PA5-59279 | Polyclonal |
WB
ICC
IHC
|
||
Proteintech Group | 17492-1-AP | Polyclonal |
WB
EL
ICC
|
||
antibodies-online | ABIN396677 | Monoclonal |
WB
EL
IHC
|
All Antibodies
Filters
Enhanced validation
Supportive data in Antibodypedia
Data presented on provider website
Data in Antibodypedia (inconclusive)
Recommended by provider
Supportive data in Antibodypedia
Data presented on provider website
Data in Antibodypedia (inconclusive)
Recommended by provider