abx004859

antibody from Abbexa

Targeting: ASL ASAL

Immunocytochemistry

Antibody data

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Validation data

Product number: abx004859 - Provider product page
Provider: Abbexa
Product name: Argininosuccinate Lyase (ASL) Antibody
Antibody type: Polyclonal
Description: ASL Antibody is a Rabbit Polyclonal antibody against ASL. This gene encodes a member of the lyase 1 family. The encoded protein forms a cytosolic homotetramer and primarily catalyzes the reversible hydrolytic cleavage of argininosuccinate into arginine and fumarate, an essential step in the liver in detoxifying ammonia via the urea cycle. Mutations in this gene result in the autosomal recessive disorder argininosuccinic aciduria, or argininosuccinic acid lyase deficiency. A nontranscribed pseudogene is also located on the long arm of chromosome 22. Alternatively spliced transcript variants encoding different isoforms have been described.
Reactivity: Human, Mouse
Host: Rabbit
Conjugate: Unconjugated
Isotype: IgG
Vial size: 100 µl
Concentration: > 1 mg/ml
Storage: Aliquot and store at -20°C. Avoid repeated freeze/thaw cycles.

ASL protein structure - abx004859 shown in red.