Tissue expression
Cell line expression
Protein structure
MCCC1
Methylcrotonoyl-CoA carboxylase 1MCCA
This gene encodes the large subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. [provided by RefSeq, Jul 2008]
Top validated antibodies |
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Proteintech Group | 14861-1-AP | 2 references | Polyclonal |
WB
EL
IP
IHC |
|
Invitrogen Antibodies | 14861-1-AP | Polyclonal |
WB
IP
IHC
OA |
||
antibodies-online | ABIN395693 | 5 references | Monoclonal |
WB
EL |
|
NovoPro Bioscience Inc. | 112543 | Polyclonal |
WB
EL
IP
IHC |
||
Atlas Antibodies | HPA008310 | Polyclonal |
WB
ICC
IHC
|
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Supportive data in Antibodypedia
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Recommended by provider
Supportive data in Antibodypedia
Data presented on provider website
Data in Antibodypedia (inconclusive)
Recommended by provider