Tissue expression
Cell line expression
Protein structure
MCCC2
Methylcrotonoyl-CoA carboxylase 2MCCB
This gene encodes the small subunit of 3-methylcrotonyl-CoA carboxylase. This enzyme functions as a heterodimer and catalyzes the carboxylation of 3-methylcrotonyl-CoA to form 3-methylglutaconyl-CoA. Mutations in this gene are associated with 3-Methylcrotonylglycinuria, an autosomal recessive disorder of leucine catabolism. Alternative splicing results in multiple transcript variants encoding distinct isoforms. [provided by RefSeq, May 2018]
Top validated antibodies |
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Proteintech Group | 12117-1-AP | 4 references | Polyclonal |
WB
EL
IP
IHC |
|
Atlas Antibodies | HPA038300 | Polyclonal |
WB
ICC
IHC
|
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Aviva Systems Biology | OAAB04039 | Polyclonal |
WB
EL
IHC
FC |
||
antibodies-online | ABIN2448019 | Polyclonal |
WB
EL
IHC
FC |
||
Abgent | AP6924c | Polyclonal |
WB
IHC
FC
|
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