ABIN405406

antibody from antibodies-online

Targeting: C4BPA C4BP

Western blot (Data presented on provider website)

Antibody Data

Product number

ABIN405406

Provider

antibodies-online

Product name

anti-Complement Component 4 Binding Protein, alpha (C4BPA) (Middle Region) antibody

Antibody type

Polyclonal

Antigen

Synthetic peptide directed towards the middle region of human C4BPA

Description

Affinity Purified

Reactivity

Human

Host

Rabbit

Antigen sequence

QVLTGKRLMQ CLPNPEDVKM ALEVYKLSLE IE
QLELQRDS ARQSTLDKEL


Epitope

Middle Region

Vial size

50 μg

Concentration

1 mg/mL

Storage

For longer periods of storage, store at -20°C

Handling

Avoid repeated freeze-thaw cycles.

References

Submitted references

A novel non-synonymous polymorphism (p.Arg240His) in C4b-binding protein is associated with atypical hemolytic uremic syndrome and leads to impaired alternative pathway cofactor activity.

Blom AM, Bergström F, Edey M, Diaz-Torres M, Kavanagh D, Lampe A, Goodship JA, Strain L, Moghal N, McHugh M, Inward C, Tomson C, Frémeaux-Bacchi V, Villoutreix BO, Goodship TH
Journal of immunology (Baltimore, Md. : 1950) 2008 May 1;180(9):6385-91