Tissue expression
Cell line expression
Protein structure
ALDH4A1
Aldehyde dehydrogenase 4 family member A1ALDH4, P5CDh
This protein belongs to the aldehyde dehydrogenase family of proteins. This enzyme is a mitochondrial matrix NAD-dependent dehydrogenase which catalyzes the second step of the proline degradation pathway, converting pyrroline-5-carboxylate to glutamate. Deficiency of this enzyme is associated with type II hyperprolinemia, an autosomal recessive disorder characterized by accumulation of delta-1-pyrroline-5-carboxylate (P5C) and proline. Alternatively spliced transcript variants encoding different isoforms have been identified for this gene. [provided by RefSeq, Jun 2009]
Top validated antibodies |
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Proteintech Group | 11604-1-AP | 4 references | Polyclonal |
WB
EL
IP
IHC |
|
LSBio | LS-C133561 | Monoclonal |
WB
EL
IHC
|
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Invitrogen Antibodies | 11604-1-AP | Polyclonal |
WB
IP
IHC
OA |
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antibodies-online | ABIN2841995 | 2 references | Polyclonal |
WB
IHC |
|
NovoPro Bioscience Inc. | 107971 | Polyclonal |
WB
EL
IP
IHC |
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Supportive data in Antibodypedia
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Recommended by provider