CPS1

gene product
The mitochondrial enzyme encoded by this gene catalyzes synthesis of carbamoyl phosphate from ammonia and bicarbonate. This reaction is the first committed step of the urea cycle, which is important in the removal of excess urea from cells. The encoded protein may also represent a core mitochondrial nucleoid protein. Three transcript variants encoding different isoforms have been found for this gene. The shortest isoform may not be localized to the mitochondrion. Mutations in this gene have been associated with carbamoyl phosphate synthetase deficiency, susceptibility to persistent pulmonary hypertension, and susceptibility to venoocclusive disease after bone marrow transplantation. [provided by RefSeq, May 2010]
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459 antibodies from 31 providers.

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Antibody
Proteintech Group
3 antibodies
Novus Biologicals
53 antibodies
Abnova Corporation
11 antibodies
Atlas Antibodies
1 antibody
antibodies-online
176 antibodies
Biorbyt
21 antibodies
Invitrogen Antibodies
9 antibodies
LifeSpan BioSciences, Inc.
50 antibodies
OriGene
5 antibodies
Boster Biological Technology
4 antibodies
Acris Antibodies GmbH
2 antibodies
HUABIO Research
1 antibody
NovoPro Bioscience Inc.
5 antibodies
Abgent
3 antibodies
Affinity Biosciences
1 antibody
Aviva Systems Biology
3 antibodies
GeneTex
7 antibodies
RabMAbs
5 antibodies
ProSci
4 antibodies
St John's Laboratory
1 antibody
NSJ Bioreagents
2 antibodies
Creative Biolabs
14 antibodies
Creative Diagnostics
3 antibodies
Abbexa
7 antibodies
Cell Signaling Technology, Inc
1 antibody
RayBiotech, Inc.
1 antibody
United States Biological
34 antibodies
Leading Biology
9 antibodies
MyBioSource
3 antibodies
Sigma-Aldrich
4 antibodies